Paget's disease-like reticulosis

Paget's disease-like reticular hyperplasia, also known as localized epidermotropic reticulosis or Woringer-Kolopp disease. In 1931 Ketren and Goodman described a clinically similar MF, apparently of multiple skin lesions of epithelial origin. In 1939 Woringer and Kolopp reported a single 6-year-old boy with a single plaque-like lesion on the arm. One of Paget's disease-like reticulohistiocytosis was proposed by Braum-Falco et al based on clinical and histological appearance. This disease is a characteristic T-cell lymphoma that occurs only in the skin and clinically manifests as plaques. Histologically, it is characterized by a single nested aggregation of atypical intraepithelial T lymphocytes.

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