Pediatric endocardial elastofibrosis

Endocardial fibroelastosis (EFE) is also known as endocardial sclerosis, and its etiology is unknown. It is a more common type of infant cardiomyopathy, also known as primary endocardial elastofibrosis, and the incidence has declined in the past decade. Congenital heart disease such as aortic constriction, aortic valve stenosis, aortic valve atresia, etc. complicated with endocardial elastic fibrous hyperplasia, which is called secondary endocardial elastic fibrous hyperplasia, and its clinical significance depends on the primary heart Malformations are not included in the scope described here. Endocardial elastofibrosis has previously been referred to as "fetal endocarditis", "sclerosing endocarditis", "endocardium myocardial elastofibrosis" and the like. The main pathological change was hyperplasia of elastic fibers and collagen fibers under the endocardium.

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