Pediatric pigmented polyp syndrome

Gastrointestinal polyposis syndrome is a disease with multiple polyposis, most of which are accompanied by extra-intestinal manifestations. According to the degree of gastrointestinal involvement, the accompanying parenteral manifestations, the presence or absence of hereditary tendencies and their different genetic methods, and the general and histological manifestations of polyps. Generally can be divided into adenoma and hamartoma polyposis syndrome two categories. Pigmented polyp syndrome is a disease in hamartoma polyposis syndrome. Hamartoma polyp syndrome contains a group of diseases characterized by certain intestinal segments being affected by an irregular mixture of some tissues. It has the characteristics of non-tumorous but tumor-like proliferation. Pigmented polyp syndrome is also called periorificial lendiginosis. In China, it is often called pigmentation-gasfrointestinal polyposis syndrome, Peutz-Jeghers syndrome (PJS). The disease is a multiple gastrointestinal polyposis with mucosa and skin pigmentation. The main clinical manifestations are repeated abdominal pain, diarrhea, anemia, intestinal obstruction, intussusception, etc., and often accompanied by malignant lesions and death. . The awareness of children with pigmented polyp syndrome should be improved to facilitate early diagnosis, appropriate treatment and follow-up.

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