Atrophic papules

This disease is also known as Dego disease, Kohlmeier-Degos syndrome, lethal cutaneous and gastrointestinal arteriolar thrombosis. This disease is a disease of the skin-gut or other organs with small arterial endometritis followed by thrombosis. The etiology is unknown, and it is believed to be related to autosomal dominant inheritance, autoimmune abnormalities, decreased fibrinolytic activity, and lentiviral infection. About 1/3 of the cases have only skin damage. About 20% of the cases involve the central nervous system, and the rare ones involve the eyes, heart, kidneys, and bladder. IgA can be significantly increased.

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