Congenital abdominal wall muscular dysplasia

Congenital abdominal wall muscular dysplasia refers to anterior abdominal wall muscular dysplasia, which is a rare congenital malformation. The most prominent feature is a skin with a very wrinkled large abdomen. Patients with the disease often have congenital malformations of the urogenital system. In 1895 Parker began to call abdominal muscle dysplasia, cryptorchidism, and congenital giant bladder "triple deformities." Because the abdomen wall muscles are absent or stunted, the abdominal wall is loose, the skin forms wrinkles, and the appearance is plum, so it is called plum dry abdomen. Osler (1901) merged deformities such as bladder dilatation, hypertrophy, hydronephrosis, ureteral dilatation, and undescended testicles, and named it Prune-Belly syndrome (PBS). Some people have also called this disease Eagle-Barrett syndrome, or lack of comprehensive abdominal wall, kettle belly syndrome, and so on.

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