Hughes-Stovin syndrome

Introduction to Hughes-Stovin Syndrome Hughes-Stovin's syndrome (Hughes-Stovin's syndrome), also known as pulmonary embolism syndrome, refers to the presence of peripheral venous thrombosis, pulmonary embolism and bronchial arterial degeneration on the basis of pulmonary aneurysms. basic knowledge The proportion of illness: 0.0005%-0.001% Susceptible people: no specific population Mode of infection: non-infectious Complications: massive hemoptysis

Causes of Hughes-Stovin Syndrome

Cause:

The cause of pulmonary aneurysm is still not fully understood. There are various hypotheses that can be classified into four aspects: infectious, congenital, syphilitic and traumatic. Infectious pulmonary aneurysm is secondary to congenital heart valve malformation, arterial catheter. There are subacute bacterial endocarditis, such as patents, which cause the emboli to fall into the lungs. It is also reported that the infectious embolus of the peripheral vein falls off and causes pulmonary embolism and pulmonary aneurysm. It is generally believed that the occurrence and persistence of pulmonary aneurysm Related to pulmonary hypertension, but also pulmonary aneurysms occur in patients without pulmonary hypertension.

Pathogenesis:

The causes of the onset of the disease have not yet been fully understood. There are various hypotheses that can be classified into four aspects: infectious, congenital, syphilitic and traumatic. Infectious pulmonary aneurysm is secondary to congenital heart valve malformation and patent ductus arteriosus. Such as subacute bacterial endocarditis, infection of the embolus and into the lungs.

Hughes-Stovin Syndrome Prevention

1. Get rid of bad habits, including pregnant women and their spouses, such as smoking, alcohol and so on.

2. Actively treat diseases affecting fetal development before pregnancy, such as diabetes, lupus erythematosus, anemia, etc.

3. Actively do prenatal checkups to prevent colds. Try to avoid using drugs that have been proven to have teratogenic effects and avoid contact with toxic and harmful substances.

Hughes-Stovin syndrome complications Complications

Concurrent hemoptysis.

Hughes-Stovin syndrome symptoms common symptoms hemoptysis visual impairment nodular venous thrombosis

The clinical course of the intrinsic can be divided into three phases:

1. Phase 1: Due to the increase of intracranial pressure due to jugular vein thrombosis, patients have headache, vomiting, visual disturbance, etc., cerebrospinal fluid pressure rises, and erythrocyte sedimentation rate increases.

2. Phase 2: Repeated thrombosis in superficial or deep veins, with fever, may have a relationship between fever and thrombosis, not due to bacteremia and splenomegaly, and antibacterial therapy is ineffective.

3. No. 3: There is a chest lesion in the main complaint of hemoptysis, and a localized nodular shadow can be seen in the chest radiograph. Because the pulmonary aneurysm is a rare disease and close to the hilum, it is easy to cast this pathological shadow. Mistaken into a neoplastic disease, hemoptysis can last for several weeks, and eventually died of massive hemoptysis due to rupture of the pulmonary aneurysm.

The diagnosis is mainly based on clinical manifestations.

Hughes-Stovin syndrome check

1. X-ray: It is characterized by isolated or multiple round shadows with different shadow diameters, uniform density, clear edges or shallow lobes; expanded and thickened blood supply artery and drainage vein connected to the shadow feeding artery and hilum Connected.

2, pulmonary angiography: pulmonary angiography is a reliable method for diagnosis, pulmonary angiography can determine the shape of the lesion, the extent and extent of involvement, to provide a basis for the choice of clinical treatment.

3. Echocardiography: Acoustic angiography and pulmonary perfusion radionuclide scanning can make a correct diagnosis, but the former can not determine the location and extent of the lesion. Although the latter can determine the location and extent of the lesion, it is impossible to observe the specific anatomical details. The use of resonance and spiral CT is superior to pulmonary angiography for correct diagnosis and anatomy.

Diagnosis and identification of Hughes-Stovin syndrome

Clinical should be differentiated from pulmonary encephalopathy. Early symptoms of pulmonary encephalopathy can be manifested as headache, dizziness, memory loss, lack of energy, and reduced working ability. Followed by different levels of disturbance of consciousness, the light is drowsiness, lethargic, and then coma. In addition, there may be various dyskinesias such as increased intracranial pressure, optic nerve head edema and stun tremor, myoclonus, generalized tonic-clonic seizures. Psychiatric symptoms can be expressed as excitement, restlessness, increased speech, hallucinations, delusions, and so on. Blood gas analysis has pulmonary dysfunction and hypercapnia; the diagnosis of neurological and mental disorders caused by other causes is excluded.

The material in this site is intended to be of general informational use and is not intended to constitute medical advice, probable diagnosis, or recommended treatments.